缬氨酰-tRNA合成酶1抗体
规格:1mg/1ml
英文名: ValRS
别名: Bat 6; Bat6; D17H6S56E; EC 6.1.1.9; G7A; Protein G7a; SYVC_HUMAN; valine tRNA ligase 1, cytoplasmic; Valine tRNA ligase; Valine--tRNA ligase; ValRS; VALYL tRNA SYNTHETASE 1; valyl tRNA synthetase 2; v
分子量: 140kDa
储存液:0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glyce
克隆类型:Polyclonal
亚型:IgG
纯化方法:affinity purified by Protein A
**原:KLH conjugated synthetic peptide derived from human ValRS
交叉反应:Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, Danio
细胞定位:
缬氨酰-tRNA合成酶1抗体产品介绍:background: Aminoacyl-tRNA synthetases catalyze the aminoacylation of tRNA by their cognate amino acid. Because of their central role in linking amino acids with nucleotide triplets contained in tRNAs, aminoacyl-tRNA synthetases are thought to be among the first proteins that appeared in evolution. The protein encoded by this gene belongs to class-I aminoacyl-tRNA synthetase family and is located in the class III region of the major histocompatibility complex. [provided by RefSeq, Jul 2008] DISEASE: The disease is caused by mutations affecting the gene represented in this entry. Disease description:A disorder due to mitochondrial respiratory chain complex d缬氨酰-tRNA合成酶1抗体efects. Clinical features are variable and include muscle weakness with hypotonia, central neurological disease with progressive external ophthalmoplegia, ptosis and ataxia, delayed psychomotor development, cardiomyopathy, abnormal liver function, facial dysmorphism, microcephaly and epilepsy. Similarity: Belongs to the class-I aminoacyl-tRNA synthetase family. Contains 1 GST C-terminal domain. Gene ID:缬氨酰-tRNA合成酶1抗体 7407 Database links: Entrez Gene: 7407 Human Entrez Gene: 22321 Mouse Entrez Gene: 25009 Rat Omim: 192150 Human SwissProt: P26640 Human SwissProt: Q9Z1Q9 Mouse SwissProt: Q04462 Rat Unigene: 520026 Human Unigene: 28420 Mouse Unigene: 12314 Rat Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
缬氨酰-tRNA合成酶1抗体产品应用:WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500 (石蜡切片需做抗原修复) not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
研究领域:细胞生物 转录调节因子 表观遗传学
储存条件: Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
来源: Rabbit
外观: Lyophilized or Liquid